Campo DC | Valor | Idioma |
dc.contributor.author | Francisco, Flávia Angélica Ferreira | - |
dc.contributor.author | Silva, Jorge Luiz Pereira e | - |
dc.contributor.author | Hochhegger, Bruno | - |
dc.contributor.author | Zanetti, Gláucia Maria Ribeiro | - |
dc.contributor.author | Marchiori, Edson dos Santos | - |
dc.creator | Francisco, Flávia Angélica Ferreira | - |
dc.creator | Silva, Jorge Luiz Pereira e | - |
dc.creator | Hochhegger, Bruno | - |
dc.creator | Zanetti, Gláucia Maria Ribeiro | - |
dc.creator | Marchiori, Edson dos Santos | - |
dc.date.accessioned | 2013-10-31T18:02:25Z | - |
dc.date.issued | 2013 | - |
dc.identifier.issn | 0954-6111 | - |
dc.identifier.uri | http://repositorio.ufba.br/ri/handle/ri/13423 | - |
dc.description | Texto completo. Acesso restrito. p. 1–9 | pt_BR |
dc.description.abstract | Pulmonary alveolar microlithiasis (PAM) is a rare genetic lung disease characterized by calcifications
within the alveoli. Mutations in the SLC34A2 gene, which encodes a type IIb sodiumphosphate
cotransporter, are responsible for this disease, leading to intra-alveolar accumulation
of phosphate that favors the formation of microliths. The hallmark of this disorder is
clinical-radiological dissociation, with typical imaging findings that correlate well with specific
pathological findings. The long-term prognosis is poor and no treatment has been discovered to
date. The aim of this review is to describe the main pathological, clinical, and imaging aspects
of PAM, ranging from its genetic basis to treatment. | pt_BR |
dc.language.iso | en | pt_BR |
dc.publisher | Respiratory Medicine | pt_BR |
dc.rights | Acesso Aberto | pt_BR |
dc.source | http://dx.doi.org/10.1016/j.rmed.2012.10.014 | pt_BR |
dc.subject | Pulmonary alveolar microlithiasis | pt_BR |
dc.subject | Pulmonary diseases | pt_BR |
dc.subject | Congenital diseases | pt_BR |
dc.subject | Computed tomography | pt_BR |
dc.title | Pulmonary alveolar microlithiasis. State-of-the-art review | pt_BR |
dc.title.alternative | Respiratory Medicine | pt_BR |
dc.type | Artigo de Periódico | pt_BR |
dc.description.localpub | Salvador | pt_BR |
dc.identifier.number | v. 107, n. 1 | pt_BR |
dc.embargo.liftdate | 10000-01-01 | - |
Aparece nas coleções: | Artigo Publicado em Periódico (Faculdade de Medicina)
|