Campo DC | Valor | Idioma |
dc.contributor.author | Silveira, Laura | - |
dc.contributor.author | Torres, Isabelle de Sousa Medeiros | - |
dc.contributor.author | Salvino, Marco A. | - |
dc.contributor.author | Follador, Ivonise | - |
dc.contributor.author | Bittencourt, Achilea Candida Lisboa | - |
dc.creator | Silveira, Laura | - |
dc.creator | Torres, Isabelle de Sousa Medeiros | - |
dc.creator | Salvino, Marco A. | - |
dc.creator | Follador, Ivonise | - |
dc.creator | Bittencourt, Achilea Candida Lisboa | - |
dc.date.accessioned | 2014-10-10T15:15:29Z | - |
dc.date.issued | 2013 | - |
dc.identifier.issn | 0193-1091 | - |
dc.identifier.uri | http://repositorio.ufba.br/ri/handle/ri/16396 | - |
dc.description | Texto completo: acesso restrito. p. 67-71 | pt_BR |
dc.description.abstract | Acquired cutis laxa (ACL) is a rare connective tissue disorder that affects the skin elastic fibers, resulting in the loss of
elasticity. In 50% of cases, this condition is associated with other diseases, particularly plasma-cell dyscrasias. This report describes a case of ACL with unusual clinical and histopathological characteristics. A 29-year-old man presented with diffuse erythematous plaques that had first appeared 5 months previously. Examination revealed multiple flaccid erythematous plaques on his trunk, neck,
and skinfolds. Immunophenotyping of bone marrow aspirate revealed 7% of monoclonal plasma cells with lambda light chain
expression. Skin biopsy histology revealed foci of interstitial granulomatous reaction. Weigert stain showed a loss of elastic fibers
in the dermis, areas with thickened fibers and elastophagocytosis. Immunohistochemistry was positive for CD68. The cutaneous
findings enabled an early diagnosis of IgG lambda monoclonal gammopathy to be made. Microscopic examination revealed an
interstitial granulomatous reaction and severe alterations in the elastic fibers that varied in intensity in the different biopsies. Curiously, little has been mentioned in the literature regarding the
presence of an interstitial granulomatous reaction in ACL. It is our belief that this reaction is secondary to the degenerative process of the elastic fibers. | pt_BR |
dc.language.iso | en | pt_BR |
dc.rights | Acesso Aberto | pt_BR |
dc.source | http://dx.doi.org/10.1097/DAD.0b013e31827bceaf | pt_BR |
dc.subject | Acquired cutis laxa | pt_BR |
dc.subject | IgG lambda monoclonal gammopathy | pt_BR |
dc.subject | Interstitial granulomatous disease | pt_BR |
dc.title | Acquired cutis laxa with an interstitial granulomatous reaction associated with IgG lambda monoclonal gammopathy | pt_BR |
dc.title.alternative | American Journal of Dermatopathology | pt_BR |
dc.type | Artigo de Periódico | pt_BR |
dc.identifier.number | v. 35, n. 4 | pt_BR |
dc.embargo.liftdate | 10000-01-01 | - |
Aparece nas coleções: | Artigo Publicado em Periódico (Faculdade de Medicina)
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